{"id":5174,"date":"2025-05-06T11:39:15","date_gmt":"2025-05-06T14:39:15","guid":{"rendered":"https:\/\/sbrv.org\/paciente\/?post_type=doenca&#038;p=5174"},"modified":"2025-05-06T11:39:17","modified_gmt":"2025-05-06T14:39:17","slug":"hemangioblastoma-vhl","status":"publish","type":"doenca","link":"https:\/\/sbrv.org\/paciente\/doencas-retina\/hemangioblastoma-vhl\/","title":{"rendered":"Hemangioblastoma e S\u00edndrome de Von Hippel-Lindau: O que \u00e9, Sintomas, Diagn\u00f3stico e Tratamentos | SBRV"},"content":{"rendered":"\n<p>\nHemangioblastomas retinianos s\u00e3o tumores vasculares benignos associados \u00e0 s\u00edndrome de Von Hippel-Lindau (VHL), podendo causar exsuda\u00e7\u00e3o e edema.\n<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">O QUE \u00c9<\/h2>\n\n\n\n<p>\nTumor vascular composto por c\u00e9lulas estromais e vasos an\u00f4malos, frequentemente m\u00faltiplos.\n<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">CAUSAS E FATORES DE RISCO<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Muta\u00e7\u00e3o no gene VHL (3p25-26)<\/li>\n\n\n\n<li>Heran\u00e7a autoss\u00f4mica dominante<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\">SINTOMAS<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Vis\u00e3o borrada por exsudatos<\/li>\n\n\n\n<li>Manchas ou escotomas<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\">DIAGN\u00d3STICO<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Retinografia e angiografia:<\/strong> les\u00f5es vasculares<\/li>\n\n\n\n<li><strong>Exame sist\u00eamico:<\/strong> detectar \u00f3rg\u00e3os afetados (renal, SNC)<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\">TRATAMENTO<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Fotocoagula\u00e7\u00e3o a laser de les\u00f5es pequenas<\/li>\n\n\n\n<li>Crioterapia e braquiterapia<\/li>\n\n\n\n<li>Observa\u00e7\u00e3o em les\u00f5es assintom\u00e1ticas<\/li>\n<\/ul>\n","protected":false},"template":"","class_list":["post-5174","doenca","type-doenca","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Hemangioblastoma e S\u00edndrome de Von Hippel-Lindau: O que \u00e9, Sintomas, Diagn\u00f3stico e Tratamentos | SBRV - SBRV - \u00c1rea do Paciente<\/title>\n<meta name=\"description\" content=\"Hemangioblastoma ocular e VHL: conhe\u00e7a a s\u00edndrome e manejo ocular. 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